Lab Investigations Details

Histiocytosis X


Alternate Name:

Test:

Chest X-ray & CT (AB), lung biopsy (AB)

Sign:

Spontaneous pneumothorax

Dd:

Tuberous sclerosis, neurofibrorriatosis,lymph angioleiomyornatosis

Phys:

Manifests as Letterer-Siwe disease, eosOophiiic granuloma and Hand-Schueller-Christian dis­ease. Aetiology unknown