Alternate Name: Idiopathic Pulmonary Fibrosis
Test:
ESR (H), Hb (N or L), S.total Ig (H), S.rheumatoid factor (+ 30%), chest X-ray (AB), radionuclide scan (AB), pulmonary function tests (AB), lung biopsy (AB)
Sign:
Clubbing, cor pulmonale, cyanosis
Dd:
Sarcoidosis, pneumoconiosis, TB, atypical pneu-monia, haematological malignancy, chronic pul-monary hypertension, radiation damage
Phys:
May occur in association with collagen vascular disorders. Aetiology unknown
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